There are a number of rarer migraine syndromes. Each of these can cause particular concern when they first have their onset. Often they need investigation to be normal before a confident diagnosis is made.


Ophthalmoplegic Migraine 

  • most attacks begin before age ten
  • more common in males 
  • unilateral headache
  • eye movement markedly affected leading to double vision
  • may last days to weeks
  • third nerve usually affected but fourth and sixth nerves can be affected



Retinal Migraine 

  • difficult to diagnose
  • monocular visual symptoms
  • not always followed by headache



Hemiplegic Migraine 

  • migraine with hemiparesis, that is weakness down one side as aura symptom
  • lasts one hour to one week or more
  • imaging normal
  • autosomal familial form associated with abnormality on chromosome 19



Basilar Migraine 

  • occurs in childhood or adolescence
  • associated visual disturbance, double vision, dizziness or unsteadiness
  • may be altered or loss of consciousness
  • frequent difficulty in diagnosis when not seen by neurologist



Migraine Aura without Headache

  • neurological deficit without headache
  • more common in men
  • more common with increasing age